English
Neonates with severe disease presenting with profound cyanosis require emergent treatment with alprostadil (prostaglandin E₁) to provide adequate pulmonary blood flow r5
Before surgery, hypoxic or hypercyanotic spells in neonates or infants are treated with comfort measures, oxygen, and medications
Usually, medications are required only for urgent treatment of hypercyanotic spells, in the setting of severe right ventricular outflow tract obstruction
Full surgical repair within the first year of life, either as primary treatment or after a palliative procedure, is the mainstay of treatment r15
Paroxysmal hypercyanotic spell
Endocarditis prophylaxis r22r23r24
Sports participation r27